Double Aortic Arch—Child
by Cynthia M. Johnson, MA
Double aortic arch is a type of vascular ring heart defect. A large artery called the aorta branches into right and left tubes, instead of just being one large tube. The 2 tubes can circle around and press the airways and the tube that brings food from the mouth to the stomach (esophagus).
Double aortic arch is a birth defect. The cause is not known.
Risk factors are not well known.
A baby may have:
It may be noticed in infancy but it is often found later.
The doctor will ask about your child’s symptoms and health history. A physical exam will be done.
Pictures may be taken of your child’s body. This can be done with:
Surgery can be done to tie off and close one of the extra branches. Symptoms may get better right away or over time.
Children will need lifelong monitoring by a doctor who treats the heart.
There are no known guidelines to prevent this health problem.
American Heart Association
Healthy Children—American Academy of Pediatrics
Canadian Cardiovascular Society
Heart and Stroke Foundation of Canada
Double aortic arch. Cove Point Foundation—Johns Hopkins University website. Available at:
...(Click grey area to select URL)
Accessed November 4, 2020.
Licari A, Manca E, et al. Congenital vascular rings: a clinical challenge for the pediatrician. Pediatr Pulmonol. 2015 May;50(5):511-524.
Vascular rings and slings. EBSCO DynaMed website. Available at: https://www.dynamed.com/condition/vascular-rings-and-slings. Accessed November 4, 2020.
Last reviewed September 2020 by EBSCO Medical Review Board Kari Kassir, MD
Last Updated: 5/7/2021
EBSCO Information Services is fully accredited by URAC. URAC is an independent, nonprofit health care accrediting organization dedicated to promoting health care quality through accreditation, certification and commendation.
This content is reviewed regularly and is updated when new and relevant evidence is made available. This information is neither intended nor implied to be a substitute for professional medical advice. Always seek the advice of your physician or other qualified health provider prior to starting any new treatment or with questions regarding a medical condition.
To send comments or feedback to our Editorial Team regarding the content please email us at firstname.lastname@example.org. Our Health Library Support team will respond to your email request within 2 business days.